{"id":2953,"date":"2022-08-08T16:24:28","date_gmt":"2022-08-08T14:24:28","guid":{"rendered":"https:\/\/dev.ircpss.com\/prise-en-charge-des-spsc\/"},"modified":"2025-11-18T09:54:05","modified_gmt":"2025-11-18T08:54:05","slug":"prise-en-charge-des-spsc","status":"publish","type":"page","link":"https:\/\/dev.ircpss.com\/fr\/prise-en-charge-des-spsc\/","title":{"rendered":"Prise en charge des SPSC"},"content":{"rendered":"<div class=\"wpb-content-wrapper\"><p>[vc_row full_width=\u00a0\u00bbstretch_row\u00a0\u00bb css=\u00a0\u00bb.vc_custom_1658395068807{background-position: center !important;background-repeat: no-repeat !important;background-size: cover !important;}\u00a0\u00bb el_class=\u00a0\u00bbheader-bg\u00a0\u00bb][vc_column offset=\u00a0\u00bbvc_hidden-xs\u00a0\u00bb][vc_empty_space height=\u00a0\u00bb100px\u00a0\u00bb][\/vc_column][\/vc_row][vc_row full_width=\u00a0\u00bbstretch_row\u00a0\u00bb css=\u00a0\u00bb.vc_custom_1658395254271{background-position: center !important;background-repeat: no-repeat !important;background-size: cover !important;}\u00a0\u00bb el_class=\u00a0\u00bbheader-bg\u00a0\u00bb][vc_column width=\u00a0\u00bb1\/12&Prime;][\/vc_column][vc_column width=\u00a0\u00bb10\/12&Prime;][vc_column_text]<\/p>\n<h1>Prise en charge des <span class=\"gradient\">shunts porto-syst\u00e9miques cong\u00e9nitaux<\/span><\/h1>\n<p>[\/vc_column_text][vc_column_text]Comme les SPSC peuvent causer des complications, la fermeture des SPSC persistants au-del\u00e0 de l&rsquo;\u00e2ge de 1 an doit \u00eatre discut\u00e9e. Il n&rsquo;existe pas de consensus international. Cependant, il est maintenant admis dans la plupart des centres que la fermeture pourrait \u00eatre r\u00e9alis\u00e9e apr\u00e8s l&rsquo;\u00e2ge de 1 ou 2 ans. Dans des cas tr\u00e8s exceptionnels, une fermeture n\u00e9onatale des SPSC extrah\u00e9patiques peut \u00eatre propos\u00e9e.   <\/p>\n<p>Avant la fermeture, un bilan complet est r\u00e9alis\u00e9 pour rechercher des complications.<\/p>\n<p>Les SPSC peuvent \u00eatre ferm\u00e9s par radiologie interventionnelle (par voie vasculaire) ou chirurgie. Selon l&rsquo;anatomie, la pression portale pendant l&rsquo;occlusion du SPSC, et le contexte, la fermeture peut \u00eatre r\u00e9alis\u00e9e en une ou deux \u00e9tapes. <\/p>\n<p>Dans de rares cas, une strat\u00e9gie d&rsquo;attente et d&rsquo;observation peut \u00eatre propos\u00e9e.<\/p>\n<p class=\"p1\">Un suivi prolong\u00e9 est n\u00e9cessaire dans tous les cas pour rechercher une complication lorsque le SPSC est perm\u00e9able et pour v\u00e9rifier l&rsquo;\u00e9volution des complications en cas de fermeture.<\/p>\n<p>[\/vc_column_text][\/vc_column][vc_column width=\u00a0\u00bb1\/12&Prime;][\/vc_column][\/vc_row][vc_row][vc_column width=\u00a0\u00bb1\/3&Prime;][vc_single_image image=\u00a0\u00bb148&Prime; img_size=\u00a0\u00bblarge\u00a0\u00bb alignment=\u00a0\u00bbcenter\u00a0\u00bb style=\u00a0\u00bbvc_box_rounded\u00a0\u00bb onclick=\u00a0\u00bblink_image\u00a0\u00bb][\/vc_column][vc_column width=\u00a0\u00bb1\/3&Prime;][vc_single_image image=\u00a0\u00bb115&Prime; img_size=\u00a0\u00bblarge\u00a0\u00bb alignment=\u00a0\u00bbcenter\u00a0\u00bb style=\u00a0\u00bbvc_box_rounded\u00a0\u00bb onclick=\u00a0\u00bblink_image\u00a0\u00bb][\/vc_column][vc_column width=\u00a0\u00bb1\/3&Prime;][vc_single_image image=\u00a0\u00bb113&Prime; img_size=\u00a0\u00bblarge\u00a0\u00bb alignment=\u00a0\u00bbcenter\u00a0\u00bb style=\u00a0\u00bbvc_box_rounded\u00a0\u00bb onclick=\u00a0\u00bblink_image\u00a0\u00bb][\/vc_column][\/vc_row][vc_row][vc_column][vc_column_text]<\/p>\n<p style=\"text-align: center;\">La radiologie interventionnelle permet le traitement mini-invasif des SPSC selon leur anatomie<\/p>\n<p>[\/vc_column_text][vc_empty_space height=\u00a0\u00bb20px\u00a0\u00bb][\/vc_column][\/vc_row][vc_row gap=\u00a0\u00bb35&Prime;][vc_column width=\u00a0\u00bb1\/2&Prime;][vc_single_image image=\u00a0\u00bb2955&Prime; img_size=\u00a0\u00bb400&#215;400&Prime; alignment=\u00a0\u00bbcenter\u00a0\u00bb style=\u00a0\u00bbvc_box_rounded\u00a0\u00bb onclick=\u00a0\u00bblink_image\u00a0\u00bb css=\u00a0\u00bb\u00a0\u00bb][vc_column_text]<\/p>\n<p style=\"text-align: center;\">L&rsquo;aspect d&rsquo;un SPSC au scanner avant et apr\u00e8s occlusion. Sur cette image, le SPSC est le gros vaisseau allant directement au c\u0153ur (fl\u00e8che jaune) sans veine porte visible allant vers la partie droite du foie avec un bouchon endovasculaire. <\/p>\n<p>[\/vc_column_text][\/vc_column][vc_column width=\u00a0\u00bb1\/2&Prime;][vc_single_image image=\u00a0\u00bb2954&Prime; img_size=\u00a0\u00bb400&#215;400&Prime; alignment=\u00a0\u00bbcenter\u00a0\u00bb style=\u00a0\u00bbvc_box_rounded\u00a0\u00bb onclick=\u00a0\u00bblink_image\u00a0\u00bb][vc_column_text]<\/p>\n<p style=\"text-align: center;\">Sur cette image, l&rsquo;aspect sur une vue comparable quelques mois apr\u00e8s fermeture par un gros bouchon plac\u00e9 dans la malformation (fl\u00e8che jaune). Notez la visibilit\u00e9 de la veine porte droite (fl\u00e8che bleue) qui s&rsquo;est d\u00e9velopp\u00e9e depuis la fermeture du SPSC. <\/p>\n<p>[\/vc_column_text][\/vc_column][\/vc_row][vc_row][vc_column][vc_empty_space height=\u00a0\u00bb20px\u00a0\u00bb][\/vc_column][\/vc_row][vc_row][vc_column width=\u00a0\u00bb1\/3&Prime;][vc_single_image image=\u00a0\u00bb135&Prime; img_size=\u00a0\u00bblarge\u00a0\u00bb alignment=\u00a0\u00bbcenter\u00a0\u00bb style=\u00a0\u00bbvc_box_rounded\u00a0\u00bb onclick=\u00a0\u00bblink_image\u00a0\u00bb][\/vc_column][vc_column width=\u00a0\u00bb1\/3&Prime;][vc_single_image image=\u00a0\u00bb109&Prime; img_size=\u00a0\u00bblarge\u00a0\u00bb alignment=\u00a0\u00bbcenter\u00a0\u00bb style=\u00a0\u00bbvc_box_rounded\u00a0\u00bb onclick=\u00a0\u00bblink_image\u00a0\u00bb][\/vc_column][vc_column width=\u00a0\u00bb1\/3&Prime;][vc_single_image image=\u00a0\u00bb105&Prime; img_size=\u00a0\u00bblarge\u00a0\u00bb alignment=\u00a0\u00bbcenter\u00a0\u00bb style=\u00a0\u00bbvc_box_rounded\u00a0\u00bb onclick=\u00a0\u00bblink_image\u00a0\u00bb][\/vc_column][\/vc_row][vc_row][vc_column][vc_column_text]<\/p>\n<p style=\"text-align: center;\">La chirurgie permet le traitement des SPSC selon leur anatomie<\/p>\n<p>[\/vc_column_text][vc_empty_space height=\u00a0\u00bb20px\u00a0\u00bb][\/vc_column][\/vc_row][vc_row][vc_column][vc_btn title=\u00a0\u00bbFind a local expert\u00a0\u00bb style=\u00a0\u00bbcustom\u00a0\u00bb custom_background=\u00a0\u00bb#4767e7&Prime; custom_text=\u00a0\u00bb#ffffff\u00a0\u00bb size=\u00a0\u00bblg\u00a0\u00bb align=\u00a0\u00bbcenter\u00a0\u00bb link=\u00a0\u00bburl:https%3A%2F%2Fircpss.com%2Fircpss-local-experts%2F|title:Find%20a%20local%20expert|\u00a0\u00bb][\/vc_column][\/vc_row][vc_row][vc_column][vc_empty_space height=\u00a0\u00bb20px\u00a0\u00bb][\/vc_column][\/vc_row]<\/p>\n<\/div>","protected":false},"excerpt":{"rendered":"<p>[vc_row full_width=\u00a0\u00bbstretch_row\u00a0\u00bb css=\u00a0\u00bb.vc_custom_1658395068807{background-position: center !important;background-repeat: no-repeat !important;background-size: cover !important;}\u00a0\u00bb el_class=\u00a0\u00bbheader-bg\u00a0\u00bb][vc_column offset=\u00a0\u00bbvc_hidden-xs\u00a0\u00bb][vc_empty_space height=\u00a0\u00bb100px\u00a0\u00bb][\/vc_column][\/vc_row][vc_row full_width=\u00a0\u00bbstretch_row\u00a0\u00bb css=\u00a0\u00bb.vc_custom_1658395254271{background-position: center !important;background-repeat: no-repeat !important;background-size: cover !important;}\u00a0\u00bb el_class=\u00a0\u00bbheader-bg\u00a0\u00bb][vc_column width=\u00a0\u00bb1\/12&Prime;][\/vc_column][vc_column width=\u00a0\u00bb10\/12&Prime;][vc_column_text] Prise en charge<span class=\"excerpt-hellip\"> [\u2026]<\/span><\/p>\n","protected":false},"author":1,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_acf_changed":false,"footnotes":""},"class_list":["post-2953","page","type-page","status-publish","hentry"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.0 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Prise en charge des SPSC - IRCPSS<\/title>\n<meta name=\"description\" content=\"Les SPSC peuvent \u00eatre ferm\u00e9s par radiologie interventionnelle ou chirurgie. 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